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KMID : 1130320130560030135
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Korean Journal of Pediatrics
2013 Volume.56 No. 3 p.135 ~ p.138
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A girl with sternal malformation/vascular dysplasia association
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Lee Na-Yong
Cho Hye-Kyung
Kim Kyung-Hyo
Park Eun-Ae
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Abstract
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Sternal malformation/vascular dysplasia association is a rare congenital dysmorphology, which has not yet been reported in Korea. Its typical clinical features include a sternal cleft covered with atrophic skin, a median abdominal raphe extending from the sternal defect to the umbilicus, and cutaneous craniofacial hemangiomata. We report a case of a full-term newborn who presented with no anomalies at birth, except for a skin defect over the sternum and a supraumbilical raphe. Multiple hemangiomas appeared subsequently on her chin and upper chest wall, and respiratory distress due to subglottic hemangioma developed during the first 2 months of life. Her symptoms were controlled with oral prednisolone administration. No respiratory distress have recurred during the 3-year follow-up period.
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KEYWORD
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Sternum, Malformation, Hemangioma
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